학술대회 안내 사전등록 안내 초록등록 안내 초록등록/관리 숙박및교통 안내


мȸ ǥ ʷ

ǥ : ȣ - 490750   150 
Long-term Results of Surgical Repair for Double-Outlet Right Ventricle with Non-committed Ventricular Septal Defect
연세대학교 의과대학 흉부외과학교실¹ , 소아과학교실²
박한기¹, 유송현¹ , 양홍석¹ , 최재영² , 박영환¹
Purpose: Double-outlet right ventricle (DORV) with non-committed ventricular septal defect (VSD), can be repaired as biventricular or univentricular physiology based on the anatomic features. But, the surgical outcome has been less satisfactory. To study the long-term outcome, we reviewed our clinical experience. Methods: From 1979 through 2003, 20 patients underwent surgical repair for DORV with non-committed VSD and concordant atrioventricular connection. Patients with atretic or hypoplastic atrioventricular valve and hypoplastic left or right ventricle were excluded. The age was 5.6 ± 6.1 (range, 0.1~22) years. Nine patients had undergone previous palliative operations (aortopulmonary shunt in five, pulmonary artery banding in four patients). Fontan operation was performed if straddling of mitral valve was present or tricuspid valve tensor apparatus spans the defect. Otherwise, biventricular repair was tried by constructing intraventricular baffling, and relieving pulmonary stenosis if indicated. Results: Biventricular repair was performed in 15 patients, and univentricular repair was performed in five patients. After biventricular repair, five patients died of heart failure and complete heart block developed in two patients. There was no operative mortality in univentricular repair group. Earlier date of operation and prolonged cardiopulmonary bypass time were risk factors for operative mortality. One patient was lost for follow-up, and other survivors were followed-up for 8.0 ± 6.5 years. During follow up, five patients required reoperation. There were two late deaths due to congestive heart failure and hypoxic brain damage after redo-Rastelli operation. Ten-year survival and freedom from reoperation rates were 64 % and 63 %, respectively. At last visit, all patients were in NYHA functional class I or II. Conclusion: The results of repair for DORV with non-committed VSD have been improved and long-term survival with good quality of life can be achieved.


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